PPoma
Definicija
PPoma is a type of pancreatic endocrine tumor (see this term) that hypersecretes pancreatic polypeptide (PP) but that does not cause a hypersecretion syndrome (is non-functioning) and instead presents with only non-specific symptoms such as weight loss, abdominal pain, jaundice, diarrhea and/or an abdominal mass, hence leading to a late diagnosis. PPoma can be associated with multiple endocrine neoplasia 1 (MEN-1; see this term).
Pretraga
Pun naziv
PPoma
Kratki naziv
-
Sinonimi
Pancreatic polypeptidoma
Orpha broj
97278
Kategorija
Podkategorija
Naziv na stranom jeziku
-
Prevalenca
Nepoznato
Nasleđivanje
Not applicable
Period početka bolesti
-
ICD 10
E16.8
OMIM
NULL
UMLS
NULL
GARD
NULL
MEDDRA
NULL
Tekstualni opis
-
Etiologija
-
Prognoza
bolest_prognoza
Diferencijalna dijagnoza
-
Tretman
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Dijagnostičke metode
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Antenatalna dijagnoza
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Epidemiologija
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Genetsko savetovanje
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Terapija
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Klinička istraživanja
-